{"id":3399,"date":"2019-10-04T22:09:09","date_gmt":"2019-10-04T19:09:09","guid":{"rendered":"http:\/\/blog.ulubat.org\/?p=3399"},"modified":"2019-10-04T22:15:28","modified_gmt":"2019-10-04T19:15:28","slug":"gizemli-bir-aritmik-sorun-brugada-sendromu","status":"publish","type":"post","link":"https:\/\/blog.ulubat.org\/index.php\/genel\/gizemli-bir-aritmik-sorun-brugada-sendromu\/","title":{"rendered":"G\u0130ZEML\u0130 B\u0130R AR\u0130TM\u0130K SORUN: BRUGADA SENDROMU"},"content":{"rendered":"\n<p>  Tarihler 4 mart 2018\u2019i g\u00f6sterirken Udinese ma\u00e7\u0131 haz\u0131rl\u0131klar\u0131n\u0131 tamamlam\u0131\u015f olan Fiorentina tak\u0131m\u0131 b\u00fcy\u00fck bir \u015fok ya\u015fam\u0131\u015f&nbsp; tak\u0131m kaptan\u0131 Davide Astori odas\u0131nda \u00f6l\u00fc bulunmu\u015ftu. Sonras\u0131nda yap\u0131lan otopside ani kardiyak \u00f6l\u00fcm tan\u0131s\u0131 konulmu\u015ftu. <\/p>\n\n\n\n<figure class=\"wp-block-image\"><img loading=\"lazy\" width=\"1024\" height=\"1024\" src=\"https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-1024x1024.jpeg\" alt=\"\" class=\"wp-image-3401\" srcset=\"https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-1024x1024.jpeg 1024w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-150x150.jpeg 150w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-250x250.jpeg 250w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-125x125.jpeg 125w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-110x110.jpeg 110w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-420x420.jpeg 420w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-768x768.jpeg 768w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\n\n\n<p>  Basketbolu takip edenlerin yak\u0131ndan tan\u0131d\u0131\u011f\u0131 bir ara T\u00fcrkiye\u2019de de oynam\u0131\u015f&nbsp; olan Conrad McRae Denver\u2019de antrenmandayken ani kardiyak \u00f6l\u00fcm nedeniyle hayat\u0131n\u0131 kaybetti. S\u0131k s\u0131k sa\u011fl\u0131k kontrollerinden ge\u00e7en sporcular\u0131 bile etkileyen -hatta \u00f6ld\u00fcren- ani kardiyak \u00f6l\u00fcmlerden biri olan Brugada Sendromu nedir?<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img loading=\"lazy\" width=\"1024\" height=\"1024\" src=\"https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-1024x1024.png\" alt=\"\" class=\"wp-image-3402\" srcset=\"https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-1024x1024.png 1024w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-150x150.png 150w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-250x250.png 250w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-125x125.png 125w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-110x110.png 110w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-420x420.png 420w, https:\/\/blog.ulubat.org\/wp-content\/uploads\/2019\/10\/image-768x768.png 768w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\n\n\n<p> &nbsp;\u0130lk defa 1992\u2019de Pedro , Ramon ve Joseph Brugada karde\u015fler taraf\u0131ndan tan\u0131mlanm\u0131\u015f olan Brugada Sendromu  gen\u00e7 ya\u015ftaki hastalarda ventrik\u00fcl aritmisi ve ani \u00f6l\u00fcmle karakterize bir sendrom olarak tan\u0131mlanm\u0131\u015ft\u0131r. Bu hastal\u0131kta elektrokardiyografi (EKG) bulgusu olarak elektrolit bozuklu\u011fu, kalp hastal\u0131\u011f\u0131, kardiyak iskemi olmaks\u0131z\u0131n V1-V3 derivasyonlar\u0131nda ST y\u00fcksekli\u011fi g\u00f6r\u00fcl\u00fcr. Genetik bir hastal\u0131kt\u0131r ve otozomal dominant kal\u0131t\u0131m g\u00f6sterir . Kalpte bulunan sodyum kanallar\u0131n\u0131n d\u00fczenlenmesinden sorumlu&nbsp; genlerdeki mutasyon hastal\u0131ktan sorumlu tutulan mekanizmad\u0131r . \u015eimdiye kadar 60 farkl\u0131 mutasyonu saptanan bu sendrom s\u0131kl\u0131kla SCN5A (%30) geninden kaynaklanmaktad\u0131r Brugada Sendromu genellikle erkeklerde g\u00f6r\u00fclmekte olup t\u00fcm ani \u00f6l\u00fcmlerin yakla\u015f\u0131k %4\u2019\u00fcnden sorumlu oldu\u011fu d\u00fc\u015f\u00fcn\u00fclmektedir . 2 g\u00fcn ile 84 ya\u015f aras\u0131 de\u011fi\u015fen tan\u0131 ya\u015f\u0131 ile birlikte, ani \u00f6l\u00fcm ortalama ya\u015f\u0131 41\u2019dir.&nbsp;  <\/p>\n\n\n\n<p> &nbsp;G\u00fcneydo\u011fu Asya\u2019da daha y\u00fcksek oranda g\u00f6r\u00fclmekte olan bu sendrom Filipinler\u2019de konu\u015fma dilinde bangungut (uykuda y\u00fckselmek ve inlemek), Japonya\u2019da pokkuri (ani ve beklenmedik olarak durma fenomeni) ve Tayland\u2019da Lai Tai (uykuda \u00f6l\u00fcm) olarak da bilinmektedir.<\/p>\n\n\n\n<p> &nbsp;&nbsp;Brugada&nbsp;Sendromunun 3 tipi bulunmaktad\u0131r (Tip 1,&nbsp;Tip 2, Tip 3)&nbsp;ve b\u00fct\u00fcn tiplerde d\u0131\u015fa do\u011fru ak\u0131mlarda potasyum art\u0131\u015f\u0131 vard\u0131r bu sebepten \u00f6t\u00fcr\u00fc&nbsp;aksiyon potansiyelinde karakteristik bir \u00e7entik ve kubbe kayb\u0131 g\u00f6zlenmektedir.&nbsp;Tip 1, Tip 2 ve Tip 3\u2019e g\u00f6re daha&nbsp;maligndir. EKG de\u011fi\u015fiklikleri&nbsp;Brugada&nbsp;Sendromu ile birlikte ge\u00e7ici olabilir ve bir\u00e7ok fakt\u00f6r taraf\u0131ndan a\u00e7\u0131\u011fa \u00e7\u0131kabilir veya artabilir: Ate\u015f,&nbsp;\u0130skemi, Bir\u00e7ok ila\u00e7&nbsp;( sodyum&nbsp;kanal&nbsp;blokerleri,&nbsp;kalsiyum kanal&nbsp;blokerleri, Alfa&nbsp;agonistler, Beta&nbsp;blokerler, Nitratlar), kokain, alkol,&nbsp;hipokalemi,&nbsp;hipotermi.&nbsp; <\/p>\n\n\n\n<figure class=\"wp-block-image\"><img src=\"https:\/\/upload.wikimedia.org\/wikipedia\/commons\/thumb\/5\/5a\/Brugada.jpg\/350px-Brugada.jpg\" alt=\"tip 1 brugada ile ilgili g\u00f6rsel sonucu\" \/><\/figure>\n\n\n\n<p>Bilinen tek tedavi ICD implatasyonudur ancak son y\u0131llarda ventrik\u00fcler ektopinin kateter ablasyonu da risk\/fayda g\u00f6zetiminde terapotik yakla\u015f\u0131m olarak literat\u00fcre girmi\u015ftir. Di\u011fer bir y\u00f6ntem de ailesinde 40 ya\u015f alt\u0131 ani \u00f6l\u00fcm g\u00f6zlenen her bireyin EKG \u00e7ektirmesi de bu sendromun proflaksisi i\u00e7in \u00f6nem arz etmektedir. <\/p>\n\n\n\n<p><\/p>\n\n\n\n<p> Brugada Sendromlu bireylere g\u00fcnl\u00fck ya\u015famda \u00f6neriler ;                                   -Brugada Sendromlu bireylerin a\u011f\u0131r sporlar yapmamas\u0131                                                   -\u00c7ok fazla alkol ve kafein t\u00fcketmemesi                                                                                -\u00c7ok so\u011fuk ve s\u0131cak ortamlarda fazla bulunmamas\u0131                                                 -Kokain kullanmamas\u0131  tavsiye edilir.                                                                      ( 22 Nisan 2019- &#8221;Egzersiz ve Kalp Sempozyumu&#8221;  \u0130zmir Katip \u00c7elebi \u00dcniversitesi )                                                                                                        <\/p>\n\n\n\n<p>      <\/p>\n\n\n\n<p>&nbsp;&nbsp;&nbsp;&nbsp;&nbsp;&nbsp;&nbsp; REFERANSLAR&nbsp;VE \u0130LER\u0130 OKUMA \u0130\u00c7\u0130N&nbsp;<\/p>\n\n\n\n<ul><li><a href=\"https:\/\/en.wikipedia.org\/wiki\/Davide_Astori\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/en.wikipedia.org\/wiki\/Davide_Astori<\/a>&nbsp;<\/li><li><a href=\"https:\/\/xn--aciltp-t9a.com\/brugada-sendromu\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/xn--aciltp-t9a.com\/brugada-sendromu<\/a>&nbsp;<\/li><li><a href=\"http:\/\/www.turkishjic.org\/archives\/archive-detail\/article-preview\/nadir-grlen-bir-olgu-brugada-sendromu\/16084\" target=\"_blank\" rel=\"noreferrer noopener\">http:\/\/www.turkishjic.org\/archives\/archive-detail\/article-preview\/nadir-grlen-bir-olgu-brugada-sendromu\/16084<\/a>&nbsp;<\/li><li><a href=\"https:\/\/www.acilci.net\/brugada-sendromu\/\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/www.acilci.net\/brugada-sendromu\/<\/a>&nbsp;<\/li><\/ul>\n\n\n\n<ul><li><a href=\"http:\/\/www.afzirvesi.org\/2018sunumlar\/SabriDemircan.pdf\" target=\"_blank\" rel=\"noreferrer noopener\">http:\/\/www.afzirvesi.org\/2018sunumlar\/SabriDemircan.pdf<\/a>&nbsp;<\/li><li><a href=\"https:\/\/www.turkiyeklinikleri.com\/article\/en-brugada-sendromunda-tani-klinik-seyir-ve-tedavi-yaklasimi-36674.html\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/www.turkiyeklinikleri.com\/article\/en-brugada-sendromunda-tani-klinik-seyir-ve-tedavi-yaklasimi-36674.html<\/a>&nbsp;<\/li><\/ul>\n","protected":false},"excerpt":{"rendered":"<p>Tarihler 4 mart 2018\u2019i g\u00f6sterirken Udinese ma\u00e7\u0131 haz\u0131rl\u0131klar\u0131n\u0131 tamamlam\u0131\u015f olan Fiorentina tak\u0131m\u0131 b\u00fcy\u00fck bir \u015fok ya\u015fam\u0131\u015f&nbsp; tak\u0131m kaptan\u0131 Davide Astori<\/p>\n","protected":false},"author":192,"featured_media":3403,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":[],"categories":[1],"tags":[],"acf":[],"views":2166,"_links":{"self":[{"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/posts\/3399"}],"collection":[{"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/users\/192"}],"replies":[{"embeddable":true,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/comments?post=3399"}],"version-history":[{"count":2,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/posts\/3399\/revisions"}],"predecessor-version":[{"id":3405,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/posts\/3399\/revisions\/3405"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/media\/3403"}],"wp:attachment":[{"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/media?parent=3399"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/categories?post=3399"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/blog.ulubat.org\/index.php\/wp-json\/wp\/v2\/tags?post=3399"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}